Alpha-heavy chain disease
Alpha-heavy chain disease
Definition
Alpha-heavy chain disease (alpha-HCD) is a type of HCD characterized by the production of incomplete monoclonal alpha-heavy chains without associated light chains. Alpha-HCD is considered to be a subtype of immunoproliferative small intestinal disease (IPSID). The clinical presentation includes chronic diarrhea with evidence of malabsorption.
Also known as alpha chain disease, Alpha heavy chain disease, Alpha-HCD, Immunoproliferative small intestinal disease, IPSID, Mediterranean abdominal lymphoma, Mediterranean lymphoma, Mediterraneanl lymphoma — per MONDO
Also identified as
- DOID 0060126 per MONDO
- MESH D007161 per MONDO
- NCIT C3132 per MONDO
- Orphanet 100025 per MONDO
- UMLS C0021071 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Alimentary part of gastrointestinal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Alimentary part of gastrointestinal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Intestine | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Intestine | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Lymphoid system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Lymphoid system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Small intestine | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Small intestine | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |