Arthrogryposis multiplex congenita
ICD-10 Code
Q74.3
Arthrogryposis multiplex congenita
Definition
Arthrogryposis multiplex congenita (AMC) is a group of disorders characterized by congenital limb contractures. It manifests as limitation of movement of multiple limb joints at birth that is usually non-progressive and may include muscle weakness and fibrosis. AMC is always associated with decreased intrauterine fetal movement which leads secondarily to the contractures.
Also known as AMC, arthrogryposis multiplex congenita, Arthromyodysplasia congenita, congenital arthromyodysplasia, multiple congenital arthrogryposis, myodysplasia — per MONDO