Primary cutaneous amyloidosis

Primary cutaneous amyloidosis

Definition

Cutaneous amyloidosis refers to a variety of skin diseases characterized histologically by the extracellular accumulation of amyloid deposits in the dermis. Rare forms include lichen amyloidosus, X-linked reticulate pigmentary disorder, primary localized cutaneous nodular amyloidosis, and macular amyloidosis.

Also known as primary localised cutaneous amyloidosis, primary localized cutaneous amyloidosis — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Integumental system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Lymphoid system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Skin of body Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Skin of body Disease Has Primary Anatomic Site NCIT · CC BY 4.0