Charcot-Marie-Tooth disease
Charcot-Marie-Tooth disease
Definition
An inherited degenerative disorder involving the peripheral nerves. It is caused by mutations in the genes that are responsible for the production of proteins necessary for the function and structure of the peripheral nerves. It is characterized by muscle atrophy and weakness in the feet, legs, hands, and arms and loss of sensation in the limbs.
Also known as Charcot Marie Tooth muscular atrophy, Charcot-Marie-Tooth disease, Charcot-Marie-Tooth hereditary neuropathy, CMT, CMT/HMSN, peroneal muscular atrophy — per MONDO
Also identified as
- DOID 10595 per MONDO
- ICD9 356.1 per MONDO
- MESH D002607 per MONDO
- NCIT C75467 per MONDO
- Orphanet 166 per MONDO
- UMLS C0007959 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |