Low anorectal malformation
Low anorectal malformation
Definition
Low anorectal malformation is a rare, genetic, non-syndromic subtype of anorectal malformation, resulting from a developmental defect during embryogenesis, characterized by a wide spectrum of anorectal anomalies lying below the ischial tuberosity (e.g., anovestibular fistula in female, perineal and anocutaneous fistulas, and anal stenosis). Patients may present with failure to pass meconium, failure to thrive, and chronic constipation.
Also identified as
- ICD9 751.5 per MONDO
- NCIT C98975 per MONDO
- Orphanet 171215 per MONDO
- SCTID 253772005 per MONDO
- UMLS C0345218 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Alimentary part of gastrointestinal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Alimentary part of gastrointestinal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Intestine | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Intestine | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Large intestine | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |