Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma

Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma

Definition

Primary cutaneous aggressive epidermotropic CD8+ T-cell lymphoma is a rare form of primary cutaneous T-cell lymphoma characterized by rapidly progressing, localized or disseminated nodules, tumors or eczematous skin lesions. It has a particularly aggressive clinical course with a high tendency to spread, in advanced stages, to extracutaneous locations (the central nervous system, lung, testes). Lymph nodes are often spared.

Also known as Berti lymphoma, primary cutaneous epidermotropic cytotoxic CD8+ T-cell lymphoma — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Integumental system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Lymphoid system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Skin of body Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Skin of body Disease Has Primary Anatomic Site NCIT · CC BY 4.0