Eosinophilic granulomatosis with polyangiitis
Eosinophilic granulomatosis with polyangiitis
Definition
Eosinophilic granulomatosis with polyangiitis (EGPA), previously known as Churg-Strauss syndrome, is a systemic vasculitis of small-to medium vessels, characterized by asthma, transient pulmonary infiltrates, and hypereosinophilia.
Also known as allergic angiitides, allergic angiitides, granulomatous, allergic angiitis, allergic angiitis and granulomatosis, allergic angiitis, granulomatous, allergic granulomatoses, allergic granulomatosis, allergic granulomatous and angiitis, allergic granulomatous Angiitides, allergic granulomatous angiitis, angiitides, allergic, angiitides, allergic granulomatous, angiitides, granulomatous allergic, angiitis, allergic, angiitis, allergic granulomatous, angiitis, granulomatous allergic, Churg Strauss Syndrome, Churg-Strauss syndrome, Churg-Strauss vasculitis, CSS, EGPA, eosinophilic granulomatous Vasculitides, eosinophilic granulomatous vasculitis, granulomatoses, allergic, granulomatosis, allergic, granulomatous allergic Angiitides, granulomatous allergic angiitis, granulomatous angiitides, allergic, granulomatous angiitis, allergic, granulomatous vasculitides, eosinophilic, granulomatous vasculitis, eosinophilic, syndrome, Churg-Strauss, vasculitides, eosinophilic granulomatous, vasculitis, Churg Strauss, vasculitis, Churg-Strauss, vasculitis, eosinophilic granulomatous — per MONDO
Also identified as
- DOID 3049 per MONDO
- ICD10CM M30.1 per MONDO
- MESH D015267 per MONDO
- NCIT C34481 per MONDO
- Orphanet 183 per MONDO
- SCTID 82275008 per MONDO
- UMLS C0008728 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |