Isolated ectopia lentis
Isolated ectopia lentis
Definition
Isolated ectopia lentis (IEL) is a rare, clinically variable, eye disorder characterized by dislocation of the lens, often causing significant reduction in visual acuity.
Also known as ectopia lentis syndrome, familial ectopia lentis, isolated lens position anomaly, nonsyndromic lens position anomaly — per MONDO
Also identified as
- DOID 0111148 per MONDO
- MESH C536184 per MONDO
- NCIT C34566 per MONDO
- Orphanet 1885 per MONDO
- SCTID 74969002 per MONDO
- UMLS C1851286 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Camera-type eye | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Lens | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |