Rasmussen subacute encephalitis
Rasmussen subacute encephalitis
Definition
A rare, progressive chronic inflammation of a single cerebral hemisphere that usually affects children. It is characterized by severe seizures, loss of motor skills and speech, hemiparesis, and dementia.
Also known as CFE, chronic focal encephalitis, Rasmussen Encephalitis, Rasmussen syndrome, Rasmussen's encephalitis, Rasmussen's syndrome — per MONDO
Also identified as
- ICD9 323.9 per MONDO
- MESH C535291 per MONDO
- NCIT C125384 per MONDO
- Orphanet 1929 per MONDO
- SCTID 230191005 per MONDO
- UMLS C2930868 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Brain | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Brain | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |