Hennekam syndrome

Hennekam syndrome

Definition

Hennekam syndrome is characterized by the association of lymphoedema, intestinal lymphangiectasia, intellectual deficit and facial dysmorphism.

Also known as Hennekam lymphangiectasia lymphedema syndrome, Hennekam lymphangiectasia-lymphedema syndrome, lymphedema-lymphangiectasia-intellectual disability syndrome — per MONDO

Also identified as