Diffuse cutaneous systemic sclerosis
Diffuse cutaneous systemic sclerosis
Definition
Diffuse cutaneous systemic sclerosis (dcSSc) is a subtype of Systemic Sclerosis (SSc) characterized by truncal and acral skin fibrosis with an early and significant incidence of diffuse involvement (interstitial lung disease, oliguric renal failure, diffuse gastrointestinal disease, and myocardial involvement).
Also known as diffuse cutaneous systemic scleroderma, dSSc, progressive cutaneous systemic scleroderma, progressive cutaneous systemic sclerosis — per MONDO