Atypical hypotonia-cystinuria syndrome

Atypical hypotonia-cystinuria syndrome

Definition

A form of hypotonia-cystinuria syndrome characterized by mild to moderate intellectual disability in addition to classic hypotonia-cystinuria syndrome phenotype (cystinuria type 1, generalized hypotonia, poor feeding, growth retardation, and minor facial dysmorphism).

Also known as atypical HCS — per MONDO

Also identified as