Progressive supranuclear palsy-progressive non-fluent aphasia syndrome
Progressive supranuclear palsy-progressive non-fluent aphasia syndrome
Definition
PSP-progressive non fluent aphasia (PSP-PNFA) is an atypical variant of progressive supranuclear palsy (PSP), a rare late-onset neurodegenerative disease. Unlike classic PSP (Richardson syndrome) patients present with an isolated speech production problem years before developing other motor features of PSP.
Also known as progressive supranuclear palsy-apraxia of speech syndrome, PSP-AOS, PSP-PNFA — per MONDO