Congenital pulmonary airway malformation
Congenital pulmonary airway malformation
Definition
An abnormality in lung development that is characterized by a multicystic mass resulting from an adenomatous overgrowth of the terminal bronchioles with a consequent reduction of pulmonary alveoli. This anomaly is classified into three types by the cyst size.
Also known as CCAM, congenital cystic adenomatoid malformation of lung, congenital cystic adenomatoid malformation of the lung, congenital cystic adenomatous malformation of the lung, congenital cystic disease of the lung, CPAM — per MONDO
Also identified as
- MESH D015615 per MONDO
- NCIT C98892 per MONDO
- Orphanet 2444 per MONDO
- SCTID 111318005 per MONDO
- UMLS C0010668 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Lungs | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Lungs | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Respiratory system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Respiratory system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |