Arrhythmogenic right ventricular cardiomyopathy
Arrhythmogenic right ventricular cardiomyopathy
Definition
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a heart muscle disease that consists in progressive dystrophy of primarily the right ventricular myocardium with fibro-fatty replacement and ventricular dilation, and that is clinically characterized by ventricular arrhythmias and a risk of sudden cardiac death.
Also known as arrhythmogenic right ventricular cardiomyopathy, arrhythmogenic right ventricular dysplasia, arrhythmogenic RVD, ARVD, right ventricular dysplasia — per MONDO