Pilocytic astrocytoma

Definition

Pilocytic astrocytoma is a rare subtype of low-grade glioma of the central nervous system characterized by a well circumscribed, often cystic, brain tumor with a discrete mural nodule and long, hair-like projections that extend from the neoplastic astrocytes. Depending on the primary localization and the size of the tumor, patients can present with signs of raised intracranial pressure (headache, vomiting, papilledema), blurred vision, decreased visual acuity, ataxia and/or nystagmus, among others. It is most commonly located in the cerebellum, but occurrence in the hypothalamus, brain stem, optic chiasma, and hemispheres has also been reported.

Also known as astrocytoma, benign, astrocytoma, pilocytic, benign, grade I astrocytic neoplasm, grade I astrocytic tumor, grade I astrocytic tumour, grade I astrocytoma, pilocytic astrocytoma — per MONDO

Also identified as

• DOID 4851 per MONDO
• NCIT C4047 per MONDO
• Orphanet 251612 per MONDO
• SCTID 763865009 per MONDO
• UMLS C0334583 per MONDO

Affected Organs