Ependymoblastoma

Ependymoblastoma

Definition

Ependymoblastoma is a rare type of primitive neuroectodermal tumor (PNET) that usually occurs in young children under the age of 2 and is histologically distinguished by the production of ependymoblastic rosettes. It is associated with an aggressive course and a poor prognosis.

Also known as embryonal tumor with abundant neuropil and true Rosettes, embryonal tumor with Multilayered Rosettes with C19MC amplification, embryonal tumor with Multilayered Rosettes, C19MC-altered, embryonal tumour with abundant neuropil and true Rosettes, embryonal tumour with Multilayered Rosettes, embryonal tumour with Multilayered Rosettes with C19MC amplification, embryonal tumour with Multilayered Rosettes, C19MC-altered, ependymoblastoma, ETMR, C19MC-altered — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Central nervous system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Central nervous system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Nervous system Disease Has Associated Anatomic Site NCIT · CC BY 4.0