Pineoblastoma
Pineoblastoma
Definition
Pineoblastoma is a rare, malignant type of supratentorial primitive neuroectodermal tumor (sPNET), found mainly in children (less than 10% of cases are reported in adults), and located in the pineal region of the brain but that can metastasize along the neuroaxis. As it is the most aggressive of the pineal parenchymal tumors, it is usually associated with a poor prognosis.
Also known as pineal gland PNET, pineal gland primitive neuroectodermal neoplasm, pineal gland primitive neuroectodermal tumor, pineal gland primitive neuroectodermal tumour, pineal PNET, pineal primitive neuroectodermal neoplasm, pineal primitive neuroectodermal tumor, pineal primitive neuroectodermal tumour, pineoblastoma, pineoblastoma (WHO grade IV), pineoblastoma, malignant, PNET of pineal gland, PNET of the pineal gland, primitive neuroectodermal neoplasm of pineal gland, primitive neuroectodermal neoplasm of the pineal gland, primitive neuroectodermal tumor of pineal gland, primitive neuroectodermal tumor of the pineal gland, primitive neuroectodermal tumour of pineal gland, primitive neuroectodermal tumour of the pineal gland — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Brain | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Brain | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Pineal gland | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Pineal gland | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |