Neurofibroma
Neurofibroma
Definition
An intraneural or extraneural neoplasm arising from nerve tissues and neural sheaths. It is composed of perineurial-like fibroblasts and Schwann cells. It usually presents as a localized cutaneous lesion and less often as a circumscribed peripheral nerve mass. Patients with neurofibromatosis type 1 present with multiple masses. Neurofibromas which arise from major nerves and plexiform neurofibromas are precursor lesions to malignant peripheral nerve sheath tumors.
Also known as neurofibroma, neurofibroma (WHO grade I), neurofibroma, benign — per MONDO
Also identified as
- DOID 962 per MONDO
- ICD9 215.9 per MONDO
- MESH D009455 per MONDO
- NCIT C3272 per MONDO
- Orphanet 252183 per MONDO
- SCTID 404029005 per MONDO
- UMLS C0027830 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Peripheral nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |