Malignant triton tumor

Definition

Malignant triton tumor (MTT) is a rare aggressive subtype of malignant peripheral nerve sheath tumor (MPNST) characterized histopathologically by focal rhabdomyoblastic differentiation.

Also known as malignant neoplasm of peripheral nerve sheath with rhabdomyosarcoma, malignant neoplasm of the peripheral nerve sheath with rhabdomyosarcoma, malignant peripheral nerve sheath neoplasm with rhabdomyosarcoma, malignant peripheral nerve sheath tumor with rhabdomyosarcoma, malignant peripheral nerve sheath tumor with rhabdomyosarcomatous differenciation, malignant peripheral nerve sheath tumour with rhabdomyosarcoma, malignant peripheral nerve sheath tumour with rhabdomyosarcomatous differenciation, malignant Triton tumor, malignant tumor of peripheral nerve sheath with rhabdomyosarcoma, malignant tumor of the peripheral nerve sheath with rhabdomyosarcoma, malignant tumour of peripheral nerve sheath with rhabdomyosarcoma, malignant tumour of the peripheral nerve sheath with rhabdomyosarcoma, MPNST with rhabdomyosarcoma, MPNST with rhabdomyosarcomatous differentiation, MTT — per MONDO

Also identified as

• DOID 6707 per MONDO
• ICD9 171.9 per MONDO
• NCIT C4335 per MONDO
• Orphanet 252212 per MONDO
• SCTID 404040002 per MONDO
• UMLS C0334616 per MONDO

Affected Organs