Angiosarcoma
Angiosarcoma
Definition
A malignant tumor arising from the endothelial cells of the blood vessels. Microscopically, it is characterized by frequently open vascular anastomosing and branching channels. The malignant cells that line the vascular channels are spindle or epithelioid and often display hyperchromatic nuclei. Angiosarcomas most frequently occur in the skin and breast. Patients with long-standing lymphedema are at increased risk of developing angiosarcoma.
Also known as angiosarcoma, angiosarcoma (disease), blood vessel sarcoma, hemangiosarcoma, hemangiosarcoma, malignant, malignant angioendothelioma, malignant hemangioendothelioma, sarcoma of blood vessel, vascular sarcoma — per MONDO
Also identified as
- DOID 0001816 per MONDO
- ICD9 171.9 per MONDO
- MESH D006394 per MONDO
- NCIT C3088 per MONDO
- Orphanet 263413 per MONDO
- SCTID 403977003 per MONDO
- UMLS C0018923 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Blood vessel | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |