Rapidly progressive glomerulonephritis
Rapidly progressive glomerulonephritis
Definition
Inflammation of the glomeruli that is characterized by a rapid loss in renal function with glomerular crescent formation observed on biopsy; it is often seen in patients with concomitant autoimmune disease, like Goodpasture's syndrome or systemic lupus erythematosus.
Also known as RPGN — per MONDO
Also identified as
- DOID 4776 per MONDO
- ICD9 580.4 per MONDO
- ICD9 582.4 per MONDO
- ICD9 583.4 per MONDO
- NCIT C35264 per MONDO
- Orphanet 280569 per MONDO
- SCTID 236392004 per MONDO
- UMLS C0221239 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Adult mammalian kidney | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Adult mammalian kidney | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Genitourinary system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Genitourinary system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Renal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Renal system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |