Pseudoxanthomatous diffuse cutaneous mastocytosis
Pseudoxanthomatous diffuse cutaneous mastocytosis
Definition
Pseudoxanthomatous diffuse cutaneous mastocytosis (PDCM) is a rare form of diffuse cutaneous mastocytosis (DCM) characterized by yellow-orange infiltrated and xanthogranuloma-like lesions with only limited blistering.
Also known as infiltrative small vesicular DCM, infiltrative small vesicular diffuse cutaneous mastocytosis, Pseudoxanthomatous DCM — per MONDO