Hereditary pheochromocytoma-paraganglioma
Hereditary pheochromocytoma-paraganglioma
Definition
Neoplasm predisposition characterized by an increased risk of paragangliomas (tumors that arise from neuroendocrine tissues distributed along the paravertebral axis from the base of the skull to the pelvis) and pheochromocytomas (paragangliomas that are confined to the adrenal medulla).
Also known as familial pheochromocytoma-paraganglioma, hereditary paraganglioma-pheochromocytoma syndrome, hereditary pheochromocytoma-paraganglioma — per MONDO