Pleomorphic rhabdomyosarcoma
Pleomorphic rhabdomyosarcoma
Definition
An aggressive malignant mesenchymal neoplasm with skeletal muscle differentiation, occurring in adults and rarely in children. The tumor is characterized by the presence of bizarre round, spindle, and polygonal cells. Clinical presentation includes a rapidly enlarging painful mass usually of the lower extremities.
Also known as pleomorphic rhabdomyosarcoma — per MONDO
Also identified as
- DOID 3250 per MONDO
- ICD9 171.9 per MONDO
- NCIT C4258 per MONDO
- Orphanet 293199 per MONDO
- SCTID 404054005 per MONDO
- UMLS C0334480 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Musculature | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Musculoskeletal system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Striated muscle tissue | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |