Primary cutaneous anaplastic large cell lymphoma

Definition

Primary cutaneous anaplastic large cell lymphoma (C-ALCL) is a rare T-cell non-Hodgkin lymphoma that affects the skin and generally shows no extracutaneous involvement at presentation. It belongs to the spectrum of primary cutaneous CD30+ lymphoproliferative disorders along with lymphomatoid papulosis with which it shares overlapping clinical and histopathologic features.

Also known as ALCL, cutaneous, anaplastic large-cell lymphoma, primary cutaneous type, C-ALCL, primary anaplastic large cell lymphoma of skin, primary anaplastic large cell lymphoma of the skin, primary C-ALCL, primary cutaneous CD30 Positive anaplastic large cell lymphoma, primary cutaneous CD30+ ALCL, primary cutaneous CD30+ anaplastic large cell lymphoma, regressive atypical histiocytosis — per MONDO

Also identified as

• MESH D054446 per MONDO
• NCIT C6860 per MONDO
• Orphanet 300865 per MONDO
• UMLS C1301362 per MONDO

Affected Organs