Splenic diffuse red pulp small B-cell lymphoma

Splenic diffuse red pulp small B-cell lymphoma

Definition

Splenic diffuse red pulp small B-cell lymphoma is a rare, indolent B-cell non-Hodgkin lymphoma characterized by abnormal proliferation of small, monomorphous, basophilic B-lymphocytes, with villous cytoplasm, in the splenic red pulp, bone marrow and peripheral blood. It typically presents in the late clinical stages with splenomegaly and moderate lymphocytosis. Cytopenias are rare and likely associated with hypersplenism.

Also known as SDRPL, splenic diffuse red pulp lymphoma — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Lymphoid system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Spleen Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Spleen Disease Has Primary Anatomic Site NCIT · CC BY 4.0