Hairy cell leukemia variant
Hairy cell leukemia variant
Definition
Hairy Cell Leukemia variant (HCL-V) is defined as a rare and indolent form of small, mature, B-cell leukemia characterized by splenomegaly, an elevated white blood cell (WBC) count and hyper-cellular bone marrow. HCL-V is more aggressive and resistant to therapy than classical HCL (HCL-C).
Also known as hairy cell leukemia variant, HCL-V, leukemic reticuloendotheliosis variant, prolymphocytic variant of hairy cell leukaemia, prolymphocytic variant of hairy cell leukemia, prolymphocytic variant of HCL — per MONDO
Also identified as
- DOID 713 per MONDO
- NCIT C7401 per MONDO
- Orphanet 300878 per MONDO
- SCTID 277568007 per MONDO
- UMLS C0349633 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Bone marrow | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Lymphoid system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Spleen | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Spleen | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |