Malignant peripheral nerve sheath tumor

Definition

Malignant peripheral nerve sheath tumor (MPNST) is a rare and often aggressive soft tissue sarcoma occurring in a wide range of anatomical sites.

Also known as Malig. periph. nerve sheath tum., malignant neoplasm of peripheral nerve sheath, malignant neurilemmoma, malignant neurilemoma, malignant neurofibroma, malignant peripheral nerve sheath neoplasm, malignant peripheral nerve sheath tumor, malignant peripheral nerve sheath tumor (morphologic abnormality), malignant peripheral nerve sheath tumor [dup] (morphologic abnormality), malignant peripheral nerve sheath tumour (morphologic abnormality), malignant peripheral nerve sheath tumour [dup] (morphologic abnormality), malignant schwannoma, malignant tumor of peripheral nerve sheath, malignant tumor of the peripheral nerve sheath, malignant tumour of peripheral nerve sheath, malignant tumour of the peripheral nerve sheath, MPNST, neurofibrosarcoma, malignant, neurogenic sarcoma, schwannoma, malignant — per MONDO

Also identified as

• DOID 5940 per MONDO
• ICD9 171.9 per MONDO
• NCIT C3798 per MONDO
• Orphanet 3148 per MONDO
• SCTID 404037002 per MONDO
• UMLS C0751690 per MONDO

Affected Organs