Primary lymphoma of the conjunctiva
Primary lymphoma of the conjunctiva
Definition
Primary lymphoma of the conjunctiva is an extremely rare clonal lymphoid proliferation of the ocular surface, with an indolent course. Clinically it presents with treatment-resistant conjunctivitis, ptosis, excessive tear production or as a painless, salmon-pink, ''fleshy'' patch, with a smooth or multinodular surface, on the bulbar conjunctiva. Histologically it is usually B-cell Non-Hodgkin lymphoma (most often extranodal marginal zone B-cell lymphoma, followed by follicular and diffuse large B-cell lymphoma), with conjunctival T-cell Non-Hodgkin lymphoma being very rare.
Also known as conjunctiva lymphoma, conjunctiva primary organ-specific lymphoma, lymphoma of conjunctiva, primary lymphoid conjunctival tumor, primary lymphoid conjunctival tumour, primary organ-specific lymphoma of conjunctiva — per MONDO
Also identified as
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Camera-type eye | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Camera-type eye | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Conjunctiva | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Conjunctiva | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Craniocervical region | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Craniocervical region | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Lymphoid system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Ocular adnexa | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Ocular adnexa | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |