Autoimmune lymphoproliferative syndrome
ICD-10 Code
D89.82
Autoimmune lymphoproliferative syndrome
Definition
Autoimmune lymphoproliferative syndrome (ALPS) is a rare, inherited disorder characterized by non-malignant lymphoproliferation, multilineage cytopenias, and a lifelong increased risk of Hodgkin's and non-Hodgkin's lymphoma.
Also known as ALPS, ALPS (autoimmune lymphoproliferative syndrome), Canale-Smith syndrome, FAS deficiency — per MONDO