Catecholaminergic polymorphic ventricular tachycardia

Catecholaminergic polymorphic ventricular tachycardia

Definition

Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a severe genetic arrhythmogenic disorder characterized by adrenergically induced ventricular tachycardia (VT) manifesting as syncope and sudden death.

Also known as bidirectional tachycardia induced by catecholamine, catecholaminergic polymorphic ventricular tachycardia, CPVT, double tachycardia induced by catecholamines, malignant paroxysmal ventricular tachycardia, multifocal ventricular premature beats, ventricular tachycardia, catecholaminergic polymorphic — per MONDO

Also identified as