Takayasu arteritis
ICD-10 Code
M31.4
Takayasu arteritis
Definition
A rare inflammatory large-vessel vasculitis primarily affecting the aorta and its major branches, but also other large vessels, causing stenosis, occlusion, or aneurysm.
Also known as aortic arch arteritis, aortic arch syndrome, Arteritis, Takayasu, cervical aortic arch, idiopathic aortitis, pharyngeal arch artery syndromic disease, Takayasu arteritis, Takayasu's arteritis, Takayasu's disease — per MONDO
Also identified as
- DOID 2508 per MONDO
- ICD10CM M31.4 per MONDO
- ICD9 446.7 per MONDO
- MESH D013625 per MONDO
- NCIT C34391 per MONDO
- NCIT C35062 per MONDO
- OMIM 207600 per MONDO
- Orphanet 3287 per MONDO
- Orphanet 99079 per MONDO
- SCTID 239937004 per MONDO
- UMLS C0039263 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Artery | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |