Infantile spasms
Infantile spasms
Definition
A rare epilepsy syndrome characterized by onset of epileptic spasms in infants between 2 and 12 months of age, and rarely up to 24 months. Infants may have no antecedent history, or a history reflecting the underlying cause. The classical triad of epileptic spasms, hypsarrhythmia and developmental stagnation or regression is historically referred to as West syndrome.
Also known as IESS, infantile epileptic spasms syndrome, infantile spasms, infantile spasms syndrome, intellectual disability-hypsarrhythmia syndrome, West syndrome, West's syndrome — per MONDO