Macular telangiectasia type 1
Macular telangiectasia type 1
Definition
A rare, acquired, macular telangiectasia characterized by unilateral (rarely bilateral) abnormally dilated and tortuous capillaries around the fovea, associated with multiple arteriolar and venular aneurysms, lipid depositions, and intra-retinal cystoid degeneration. It leads to vision loss due to macular edema with hard exudates.
Also known as aneurysmal telangiectasia, idiopathic macular telangiectasia type 1, visible and exudative idiopathic juxtafoveolar retinal telangiectasis — per MONDO