Hydroa vacciniforme-like lymphoma

Definition

A rare, EBV-positive cutaneous T-cell lymphoproliferative disorder, composed of CD8 positive cytotoxic T-lymphocytes. It affects children, almost exclusively in Latin America and Asia. Patients present with papulovesicular skin lesions, clinically resembling hydroa vacciniforme, in areas of sun-exposed skin.

Also known as angiocentric cutaneous T-cell lymphoma of childhood, hV-like lymphoma, HVLL, hydroa vacciniforme-like cutaneous T-cell lymphoma, hydroa vacciniforme-like lymphoma, hydroa vacciniforme-like lymphoproliferative disorder, hydroa-like cutaneous T-cell lymphoma — per MONDO

Also identified as

• NCIT C45327 per MONDO
• Orphanet 364039 per MONDO
• SCTID 763719001 per MONDO
• UMLS C1708397 per MONDO

Affected Organs