Hypocomplementemic urticarial vasculitis
Hypocomplementemic urticarial vasculitis
Definition
Hypocomplementemic urticarial vasculitis (HUV) is an immune complex-mediated small vessel vasculitis characterized by urticaria and hypocomplementemia (low C1q with or without low C3 and C4), and usually associated with circulating anti-C1q autoantibodies. Arthritis, pulmonary disease, ocular inflammation, and glomerulonephritis are common systemic manifestations.
Also known as anti-C1q vasculitis, Mac Duffie hypocomplementemic urticarial vasculitis, Mac Duffie syndrome, McDuffie hypocomplementemic urticarial vasculitis, McDuffie syndrome — per MONDO