Extraskeletal Ewing sarcoma
Extraskeletal Ewing sarcoma
Definition
A rare malignant neoplasm of the soft tissues. It is typically a disease of children and young adults. Most commonly occurs in the paravertebral region, chest wall, pelvis and lower extremities. Treatment includes local excision with consideration for post-operative chemotherapy and/or radiotherapy.
Also known as EOE, Extra-osseous Ewing's sarcoma, extraosseous Ewing sarcoma, extraosseous Ewing tumor, extraosseous Ewing tumour, extraosseous Ewing's sarcoma, extraosseous Ewing's tumor, extraosseous Ewing's tumour, extraskeletal Ewing sarcoma, extraskeletal Ewing tumor, extraskeletal Ewing tumour, extraskeletal Ewing's sarcoma — per MONDO