Schnitzler syndrome

Schnitzler syndrome

Definition

A rare, underdiagnosed disorder in adults characterized by recurrent febrile rash, bone and/or joint pain, enlarged lymph nodes, fatigue, a monoclonal IgM component, leukocytosis and systemic inflammatory response.

Also known as chronic urticaria with gammopathy, chronic urticaria with macroglobulinemia — per MONDO

Also identified as