Langerhans cell histiocytosis

Definition

Langerhans cell histiocytosis (LCH) is a systemic disease associated with the proliferation and accumulation (usually in granulomas) of Langerhans cells in various tissues.

Also known as histiocytosis X, Langerhans cell granulomatosis, Langerhans cell histiocytosis, Langerhans cell histiocytosis, NOS, Langerhans cell histiocytosis, Not otherwise specified, LCH — per MONDO

Also identified as

• DOID 2571 per MONDO
• ICD9 202.5 per MONDO
• ICD9 277.89 per MONDO
• NCIT C3107 per MONDO
• OMIM 604856 per MONDO
• Orphanet 389 per MONDO
• SCTID 65399007 per MONDO
• UMLS C0019621 per MONDO