Mucinous adenocarcinoma of the appendix

Mucinous adenocarcinoma of the appendix

Definition

Mucinous adenocarcinoma of the appendix is a very rare, slow growing, well-differentiated epithelial neoplasm of the appendix characterized by abundant mucin production. Clinically, it presents as acute appendicitis (with abdominal pain, fever, leukocytosis) or as pseudomyxoma peritonei (wide-spread presence of mucin within the peritoneal cavity), however some patients may be completely asymptomatic at the time of diagnosis. In many cases, a second gastrointestinal malignancy is present.

Also known as appendiceal mucinous adenocarcinoma, appendix mucinous adenocarcinoma, vermiform appendix mucinous adenocarcinoma — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Alimentary part of gastrointestinal system Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Alimentary part of gastrointestinal system Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Appendix Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Appendix Disease Has Primary Anatomic Site NCIT · CC BY 4.0