Congenital adrenal hyperplasia
Congenital adrenal hyperplasia
Definition
Congenital adrenal hyperplasia (CAH) is an inherited endocrine disorder caused by a steroidogenic enzyme deficiency that is characterized by adrenal insufficiency and variable degrees of hyper or hypo androgyny manifestations, depending of the type and the severity of the disease.
Also known as adrenal hyperplasia, congenital, CAH, congenital adrenal gland hyperplasia — per MONDO
Also identified as
- DOID 0050811 per MONDO
- ICD9 255.2 per MONDO
- MESH D000312 per MONDO
- NCIT C34360 per MONDO
- Orphanet 418 per MONDO
- SCTID 237751000 per MONDO
- UMLS C0001627 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Adrenal glands | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Adrenal glands | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Endocrine gland | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
Drugs indicated
| Drug | Relation | Source |
|---|---|---|
| Hydrocortisone | may treat | MEDRT · Public domain (U.S. Government work) |