Pulmonary veno-occlusive disease and/or pulmonary capillary haemangiomatosis
Pulmonary veno-occlusive disease and/or pulmonary capillary haemangiomatosis
Definition
A rare subgroup of pulmonary arterial hypertension (PAH) characterized by obliterative fibrosis of the small pulmonary veins and venules and/or capillary infiltration of the pulmonary interstitium leading to increased pulmonary vascular resistance and right ventricular dysfunction.
Also known as PVOD and/or PCH — per MONDO