Ectopia cordis
Ectopia cordis
Definition
A rare congenital anomaly where the heart is formed outside of the thoracic cavity. It is associated with intracardiac lesions and other structural malformations.
Also known as ectopia cordis, ectopia cordis (disease) — per MONDO
Also identified as
- ICD9 746.87 per MONDO
- MESH D054083 per MONDO
- NCIT C111643 per MONDO
- Orphanet 448270 per MONDO
- SCTID 78250005 per MONDO
- UMLS C0013580 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Cardiovascular system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Cardiovascular system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |