Castleman-Kojima disease

Castleman-Kojima disease

Definition

A clinicopathologic variant of multicentric Castleman's disease characterized by thrombocytopenia, ascites (anasarca), microcytic anemia, myelofibrosis, renal dysfunction, and organomegaly

Also known as TAFRO syndrome, thrombocytopenia-anasarca-fever-renal insufficiency-organomegaly syndrome — per MONDO

Also identified as