IgG4-related retroperitoneal fibrosis

Definition

Retroperitoneal fibrosis (RPF) is characterized by the development of a fibrotic mass surrounding retroperitoneal structures, such as aorta, vena cava, ureters and psoas muscle.

Also known as idiopathic retroperitoneal fibrosis, Ormond disease, Retroperitoneal Fibrosis — per MONDO

Also identified as

• ICD9 593.4 per MONDO
• MESH D012185 per MONDO
• NCIT C26876 per MONDO
• Orphanet 49041 per MONDO
• SCTID 197808006 per MONDO
• UMLS C0035357 per MONDO