Craniopharyngioma
Craniopharyngioma
Definition
A benign, partly cystic, epithelial tumor of the sellar region, presumably derived from Rathke pouch epithelium. It affects mainly children and young adults. There are two clinicopathological forms: adamantinomatous craniopharyngioma and papillary craniopharyngioma. The most significant factor associated with recurrence is the extent of surgical resection, with lesions greater than 5 cm in diameter carrying a markedly worse prognosis. (Adapted from WHO)
Also known as craniopharyngioma (morphologic abnormality), craniopharyngioma (WHO grade I), craniopharyngioma, benign, neoplasm of Rathke's pouch, Rathke pouch neoplasm, Rathke pouch tumor, Rathke pouch tumour, Rathke's pouch neoplasm, Rathke's pouch tumor, Rathke's pouch tumour, tumor of Rathke's pouch, tumour of Rathke's pouch — per MONDO
Also identified as
- DOID 3840 per MONDO
- ICD9 237.0 per MONDO
- MESH D003397 per MONDO
- NCIT C2964 per MONDO
- Orphanet 54595 per MONDO
- SCTID 189179009 per MONDO
- UMLS C0010276 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Brain | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Brain | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Central nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Head | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |