McCune-Albright syndrome
McCune-Albright syndrome
Definition
McCune-Albright syndrome (MAS) is classically defined by the clinical triad of fibrous dysplasia of bone (FD), cafe-au-lait skin spots, and precocious puberty (PP).
Also known as Albright's disease, gonadotropin-independent female-limited sexual precocity, MAS, McCune Albright Syndrome, mccune-albright syndrome, somatic, mosaic — per MONDO
Also identified as
- DOID 1858 per MONDO
- NCIT C48627 per MONDO
- OMIM 174800 per MONDO
- Orphanet 562 per MONDO
- SCTID 726029005 per MONDO
- UMLS C0242292 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Endocrine gland | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |