Craniorachischisis
ICD-10 Code
Q00.1
Craniorachischisis
Definition
Craniorachischisis is the most severe form of neural tube defect in which both the brain and spinal cord remain open to varying degrees. It is a very rare congenital malformation of the central nervous system.
Also known as cranial rachischisis, craniorachischisis, craniorachischisis (disease) — per MONDO
Also identified as
- ICD10CM Q00.1 per MONDO
- ICD9 740.1 per MONDO
- NCIT C98907 per MONDO
- Orphanet 63260 per MONDO
- SCTID 32219008 per MONDO
- UMLS C0152426 per MONDO
Affected Organs
| Organ | Involvement | Source |
|---|---|---|
| Nervous system | Disease Has Associated Anatomic Site | NCIT · CC BY 4.0 |
| Nervous system | Disease Has Primary Anatomic Site | NCIT · CC BY 4.0 |