IgG4-related thyroid disease

IgG4-related thyroid disease

Definition

Riedel thyroiditis is a fibroinflammatory disorder of the thyroid gland, occurring more frequently in females, characterized a large, hard thyroid mass, and presenting with pressure symptoms (breathing difficulB,ties and dysphagia) or voice hoarseness and aphonia (impingement of recurrent laryngeal nerve). It can often be associated with extracervical fibroinflammatory disorders such as retroperitoneal fibrosis, primary scleroisng cholangitis and autoimmune diseases such as Hashimoto struma, Addison disease, and Biermer disease.

Also known as Riedel disease, Riedel fibrosing thyroiditis, Riedel thyroiditis, Riedel's fibrosing thyroiditis — per MONDO

Also identified as

Affected Organs

Organ Involvement Source
Craniocervical region Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Craniocervical region Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Endocrine gland Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Neck Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Neck Disease Has Primary Anatomic Site NCIT · CC BY 4.0
Thyroid gland Disease Has Associated Anatomic Site NCIT · CC BY 4.0
Thyroid gland Disease Has Primary Anatomic Site NCIT · CC BY 4.0